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dc.contributor.authorDesmoid Tumor Working Groupen_US
dc.date.accessioned2021-01-15T10:07:48Z
dc.date.issued2020-03
dc.identifier.citationEuropean journal of cancer (Oxford, England : 1990), 2020, 127 pp. 96 - 107
dc.identifier.issn0959-8049
dc.identifier.urihttps://repository.icr.ac.uk/handle/internal/4285
dc.identifier.eissn1879-0852
dc.identifier.doi10.1016/j.ejca.2019.11.013
dc.description.abstractDesmoid tumor (DT; other synonymously used terms: Desmoid-type fibromatosis, aggressive fibromatosis) is a rare and locally aggressive monoclonal, fibroblastic proliferation characterised by a variable and often unpredictable clinical course. Previously surgery was the standard primary treatment modality; however, in recent years a paradigm shift towards a more conservative management has been introduced and an effort to harmonise the strategy amongst clinicians has been made. We present herein an evidence-based, joint global consensus guideline approach to the management of this disease focussing on: molecular genetics, indications for an active treatment, and available systemic therapeutic options. This paper follows a one-day consensus meeting held in Milan, Italy, in June 2018 under the auspices of the European Reference Network for rare solid adult cancers, EURACAN, the European Organisation for Research and Treatment of Cancer (EORTC) Soft Tissue and Bone Sarcoma Group (STBSG) as well as Sarcoma Patients EuroNet (SPAEN) and The Desmoid tumour Research Foundation (DTRF). The meeting brought together over 50 adult and pediatric sarcoma experts from different disciplines, patients and patient advocates from Europe, North America and Japan.
dc.formatPrint-Electronic
dc.format.extent96 - 107
dc.languageeng
dc.language.isoeng
dc.rights.urihttps://creativecommons.org/licenses/by-nc-nd/4.0
dc.subjectDesmoid Tumor Working Group
dc.subjectHumans
dc.subjectFibromatosis, Aggressive
dc.subjectCombined Modality Therapy
dc.subjectConsensus
dc.subjectAdult
dc.subjectChild
dc.subjectDisease Management
dc.subjectPractice Guidelines as Topic
dc.titleThe management of desmoid tumours: A joint global consensus-based guideline approach for adult and paediatric patients.
dc.typeJournal Article
dcterms.dateAccepted2019-11-16
rioxxterms.versionofrecord10.1016/j.ejca.2019.11.013
rioxxterms.licenseref.urihttps://creativecommons.org/licenses/by-nc-nd/4.0
rioxxterms.licenseref.startdate2020-03
rioxxterms.typeJournal Article/Review
dc.relation.isPartOfEuropean journal of cancer (Oxford, England : 1990)
pubs.notesNot known
pubs.organisational-group/ICR
pubs.organisational-group/ICR/Primary Group
pubs.organisational-group/ICR/Primary Group/ICR Divisions
pubs.organisational-group/ICR/Primary Group/ICR Divisions/Clinical Studies
pubs.organisational-group/ICR/Primary Group/ICR Divisions/Clinical Studies/Clinical and Translational Sarcoma
pubs.organisational-group/ICR/Primary Group/ICR Divisions/Clinical Studies/Sarcoma Clinical Trials
pubs.publication-statusPublished
pubs.volume127
pubs.embargo.termsNot known
icr.researchteamClinical and Translational Sarcomaen_US
icr.researchteamSarcoma Clinical Trialsen_US
dc.contributor.icrauthorMessiou, Christinaen
dc.contributor.icrauthorJudson, Ianen
dc.contributor.icrauthorHusson, Olgaen


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