Epithelioid malignant peripheral nerve sheath tumor arising in schwannoma.
Date
2020-08-01ICR Author
Author
Heatley, N
Kolson Kokohaare, E
Strauss, DC
Hallin, M
Jones, RL
Fisher, C
Thway, K
Type
Journal Article
Metadata
Show full item recordAbstract
Epithelioid malignant peripheral nerve sheath tumor (EMPNST, malignant epithelioid schwannoma) is a rare variant of malignant peripheral nerve sheath tumor that has morphologic and immunophenotypic overlap with a variety of epithelioid neoplasms. Because of its rarity it may be potentially underrecognized. We describe a case arising in the subcutis of the thigh in a 25 year-old female, and discuss the pathologic features and differential diagnosis.
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Subject
Epithelioid malignant peripheral nerve sheath tumor
SMARCB1/INI1 gene
extremity
sarcoma
schwannoma
thigh
Language
eng
Date accepted
2020-06-18
License start date
2020-08-01
Citation
Rare Tumors, 2020, 12 pp. 2036361320950862 -
Publisher
SAGE PUBLICATIONS LTD